Cas No.: | 25518-54-1 |
Chemical Name: | 1-Propanaminium,3-carboxy-N,N,N-trimethyl-2-[(1-oxododecyl)oxy]-, inner salt, (2R)- |
Synonyms: | 1-Propanaminium,3-carboxy-N,N,N-trimethyl-2-[(1-oxododecyl)oxy]-, inner salt, (2R)-;(2R)-3-Carboxy-N,N,N-trimethyl-2-[(1-oxododecyl)oxy]-1-propanaminium inner salt;L-Carnitine dodecanoyl ester;C12-Carnitine;Dodecanoyl-L-carnitine |
SMILES: | CCCCCCCCCCCC(OC(C[N+](C)(C)C)CC([O-])=O)=O |
Formula: | C19H37NO4 |
M.Wt: | 343.501386404037 |
Purity: | >98% |
Sotrage: | 2 years -20°C Powder, 2 weeks 4°C in DMSO, 6 months -80°C in DMSO |
Description: | Dodecanoylcarnitine is present in fatty acid oxidation disorders such as long-chain acyl CoA dehydrogenase deficiency, carnitine palmitoyltransferase I/II deficiency, and is also associated with celiac disease. |
Target: | Human Endogenous Metabolite |
References: | [1]. Shigematsu Y, et al. Selective screening for fatty acid oxidation disorders by tandem mass spectrometry: difficulties in practical discrimination. J Chromatogr B Analyt Technol Biomed Life Sci. 2003 Jul 15;792(1):63-72. |